본 논문은 2페이지의 미리보기를 제공합니다. 열람(저장) 및 출력용으로 사용가능하며 편집은 불가능 합니다.
  • 17 a-Hydroxylase 결핍으로 인한 남성가성반음양 1 예
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영문초록

A 21-year-old phenotypic female with 46,XY genotype presented with primary amenorrhea, headache, absence of secondary sex characteristics, and hypertension. Further evaluation confirmed male pseudohermaphroditism having no nterus and adnexase. After basic hormonal study and ACTH stimulation test, we concluded 17 a-hydroxylase deficiency. Owing to the high risk of gonadal neoplasia in XY gonadal streaks, prophylactic removal of the steaks is recommended. Traditionally this procedure has been performed by laparotomy, but in this case laparoscopic gonadctomy was performed. Following treatment with hydrocrtisone, potassium, progesterone, 11-deoxycorticosterone, corticosterone and urinay pregnanediol levels were normalized. normal blood pressure measurements were achieved during treatment with hydrocortisone and estrogen with the patient. We report this case with a breif review of the literatures.

국문초록

저자들은 최근에 21세된 46,XY핵형을 가진 외형상 여자환자에서 17 a-hydroxylase 결핍에 의한 남성가성반음양중 1예를 경험하였기에 간단한 문헌고찰과 함께 보고하는 바이다.
  • 가격4,500
  • 페이지수6 페이지
  • 발행년1997
  • 학회명대한산부인과학회
  • 저자김재훈(JH Kim),최소영(SY Choi),김장흡(JH Kim),김진홍(CH Kim),나종구(JG Na),강창석(CS Kang)
  • 파일형식아크로뱃 뷰어(pdf)
  • 자료번호#211345
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